Immunodeficiency associated with laevocardia, bronchiectasis, and paranasal sinus anomalies.
نویسنده
چکیده
In a case of laevocardia, bronchiectasis, and paranasal sinus abnormalities, assessment on 2 occasions showed the presence of moderate immunodeficiency. Serum concentrations of IgG and IgM were low, and serum and salivary IgA was not detected. T-lymphocytes were reduced in number and cell-mediated immunity in vivo and in vitro was impaired. Opsonisation, complement system, and neutrophil functions were normal.
منابع مشابه
Recurrent pneumonias and bronchiectasis associated a commom variable immunodeficiency
Introduction Commom variable immunodeficiency (CVI) is the second more comom cause of Immunodeficiency. Its prevalence is about 10 000 a 50 000 persons. Its incidente is about the first and second life’s decade. Both genders are commited and it can be associated a several phenotypes such a recurrent inlfections,autoimmunity,enteropathy,neoplasms,polyclonal lymphocytic infiltration. The main rec...
متن کاملتعیین میزان هم‌خوانی آندوسکوپی تشخیصی و توموگرافی کامپیوتری در تشخیص بیماری‌ها و ناهنجاری‌های بینی و سینوس‌های صورت و تعیین فراوانی این ناهنجاری‌ها
CT scan is the best method in the diagnosis of paranasal sinus diseases. The object of the present study was to show the efficiency of diagnostic endoscopy in diagnosing nasal paranasal sinus diseases and anomalies. If this method proves to be accurate, patients who refuse surgery can be diagnosed, managed and followed up through a reliable method that is cost-effective and de...
متن کاملBilateral Total Aplasia of Paranasal Sinuses : A Rare Case Report
Paranasal sinus anatomical anomalies with unknown etiology are common. Paranasal sinus–related diseases are associated with so high rate of morbidities, it becomes essential to identify the structure and pathophysiology of the paranasal sinuses. Computed tomography (CT) is a valuable tool in displaying its anatomy, any anatomic variations and diseases. As paranasal sinus development is a comple...
متن کاملReduced immunoglobulin M is associated with sinus mucosal thickening, osteitis and sinus surgery in patients with common variable immunodeficiency.
BACKGROUND Although common variable immunodeficiency (CVID) is associated with sinopulmonary disease, there are no previous systematic evaluations comparing computed tomographic (CT) sinus imaging with immunoglobulin measurements in patients with this condition. METHODS We performed a retrospective review by a blinded observer using the Lund-Mackay numerical scoring scale as well as a visual ...
متن کاملUpper airway 2: Bronchiectasis, cystic fibrosis and sinusitis.
The nose and paranasal sinuses are contiguous with the lower respiratory tract. Patients with bronchiectasis and cystic fibrosis commonly have sinonasal disease, which is thought to have the same aetiology and pathophysiology as the chronic lung disease. Despite this, the conditions are rarely considered together and there is very little literature on the treatment of sinonasal disease in bronc...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Archives of disease in childhood
دوره 53 10 شماره
صفحات -
تاریخ انتشار 1978